Quick Answer: Which Primary Factor Is Responsible For Multiple Clinical Manifestations Of Cystic Fibrosis?

Which complication is appropriate in the child with cystic fibrosis?

The mucus causes problems in the lungs, pancreas, and other organs.

People with cystic fibrosis (SIS-tik fye-BROH-sis) get lung infections often.

Over time, they have more trouble breathing.

They also have digestive problems that make it hard to gain weight..

Are there different levels of cystic fibrosis?

Are there different types of cystic fibrosis? There are over 2,000 identified mutations of the cystic fibrosis gene. Cystic fibrosis is a very complex condition that affects people in different ways. Some suffer more with their digestive system than the lungs.

What clinical manifestations in the child would the nurse relate to asthma?

When identifying asthma in children you might notice signs of respiratory distress. The child may have a costal/intercostal recession or tracheal tug. Nasal flaring or head bobbing in younger children may also be apparent (PCH 2018). Upon auscultation of the chest, reduced air entry and/or wheezing may be heard.

Which factor is appropriate for possible multiple clinical manifestations in cystic fibrosis?

Which factor is appropriate for possible multiple clinical manifestations in cystic fibrosis? Children with cystic fibrosis have thick exocrine gland secretions. The viscous secretions obstruct small passages in organs such as the lungs and pancreas.

What are the 3 most common types of mutations that cause cystic fibrosis?

The most recent classification system groups mutations by the problems that they cause in the production of the CFTR protein:Protein production mutations (Class 1)Protein processing mutations (Class 2)Gating mutations (Class 3)Conduction mutations (Class 4)Insufficient protein mutations (Class 5)

At what age is cystic fibrosis usually diagnosed?

Most children are now screened for CF at birth through newborn screening and the majority are diagnosed by age 2. However, some people with CF are diagnosed as adults. A doctor who sees the symptoms of CF will order a sweat test and a genetic test to confirm the diagnosis.

How is cystic fibrosis treated or managed?

Treatments for cystic fibrosis antibiotics to prevent and treat chest infections. medicines to make the mucus in the lungs thinner and easier to cough up. medicines to widen the airways and reduce inflammation. special techniques and devices to help clear mucus from the lungs.

What is the earliest postnatal manifestation of cystic fibrosis?

Early signs of CF include: Salty sweat; many parents notice a salty taste when kissing their child. Poor growth and weight gain (failure to thrive) Constant coughing and wheezing.

Do babies with cystic fibrosis sleep more?

Children with cystic fibrosis (CF) have less sleep and more sleep interruptions than healthy children, even when the disease is well-managed and stable, an Australian study indicates.

What is the most appropriate nursing intervention for a child after tonsillectomy?

Effective nursing measurements for relieving post tonsillectomy pain include: decreasing children’s anxiety through children and their families’ psychological preparation by nurses and other caregivers, using cold compress to reduce neck and jaw pain, presenting distraction techniques, offering fluids and cold foods …

What are common signs of a pneumothorax in a child with cystic fibrosis?

The most common symptoms include:Sharp, stabbing type chest pain that may spread to the shoulder and back.Shortness of breath or difficulty breathing.Fast, shallow, breathing.

Can cystic fibrosis be missed at Birth?

Newborn screening is very sensitive and should recognise infants with inconclusive diagnosis, some of whom will go on to develop features of cystic fibrosis. However, newborn screening is not perfect and cases of CF will be missed occasionally.

What gender is cystic fibrosis most common in?

Cystic fibrosis affects both males and females; approximately 30,000 people in the United States have been diagnosed with the condition.

What famous person has cystic fibrosis?

List of people diagnosed with cystic fibrosisNameLifeGunnar Esiason(1991—)Bob Flanagan(1952–1996)Travis Flores(1991—)Nolan Gottlieb(1982—)25 more rows

What are common signs of a pneumothorax in a child with cystic fibrosis quizlet?

Signs of a pneumothorax in a child with cystic fibrosis include tachypnea, tachycardia, dyspnea, and cyanosis.

Can you have a mild case of cystic fibrosis?

Atypical CF is a milder form of the CF disorder, which is associated with mutations of the cystic fibrosis transmembrane receptor gene. Instead of having classic symptoms, individuals with atypical CF might only have mild dysfunction in 1 organ system and might or might not have elevated sweat chloride levels.

What is the end stage of cystic fibrosis?

Common symptoms at the end of life include dyspnea, fatigue, anxiety, anorexia, pain, and cough (see Fast Facts #27, 199, 200). Care providers must balance benefit versus burden of disease-specific treatments such as nebulized medications, NIPPV, and chest physiotherapy.

What do stools look like with cystic fibrosis?

Because of CF’s effects on the digestive system, a child with CF may have these symptoms: Frequent, bulky, greasy stools. A rare condition where the end part of the bowels comes out of the anus (rectal prolapse) A bowel blockage caused by a baby’s thick and sticky first bowel movement (meconium ileus)